This medication is similar to n-acetylglutamate (NAG), prescribed for hyperammonemia due to the deficiency of the liver enzyme named as N-acetylglutamate synthase (NAGS). It acts as a replacement for NAG.

None.

Adult- PO- The recommended initial dose is 100 mg/kg/day to 250 mg/kg/day.

It comes as a tablet to take by mouth, immediately before meals.

• Caution needed for patients with any allergy, during pregnancy and breastfeeding.

• Follow the diet program as directed by your healthcare provider.

•   Most Common : Vomiting, abdominal pain, fever, tonsilitis, anemia, ear infection, diarrhea, throat inflammation, and headache.
•   Blood : Anemia.
•   ENT : Ear infection.
•   Gastrointestinal : Abdominal pain, diarrhea, vomiting, difficulty in swallowing.
•   General : Weakness, fever.
•   Infections : Infection, throat inflammation, pneumonia.
•   Metabolic : Loss of appetite, hemoglobin decreased, weight decreased.
•   Central Nervous System : Headache, drowsiness.
•   Skin : Rash.

Avoid excess dosage.

Store it in refrigerator 2 - 8°C.