Last Updated on Mar 12, 2016

About

Dandy-Walker syndrome (DWS) or Dandy-Walker complex is a congenital brain malformation that involves the cerebellum (an area at the back of the brain that controls movement) and the fluid-filled spaces around it.

Dandy-Walker malformation was first described by Dandy and Blackfan in 1914.

The part of the brain located between the two cerebellar hemispheres called cerebral vermis becomes partially or completely absent. Other key features include an enlargement of the fourth ventricle (one of four connected cavities in the brain) and cyst formation near the internal base of the skull. The three features form a triad.

Dandy Walker Syndrome

It is a genetically sporadic disorder. Dandy-Walker syndrome occurs one in every 25,000 live births. Females are mostly affected.

An increase in size and pressure occurs in the fluid spaces surrounding the brain.

References:

  1. National Institute of Neurological Disorders and Stroke, "NINDS Dandy-Walker Syndrome Information Page
  2. Harrison's Principles of Internal Medicine, 17th Ed.
  3. Volpe, Joseph, J.Neurology of the Newborn, 4th edition.

Latest Publications and Research on Dandy Walker Syndrome

Comments

ganesh7432 Thursday, June 6, 2013

after treatment how many years life

Most Popular on Medindia